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Klippel-Trenaunay综合征(Klippel-Trenaunay syndrome,KTS)是少见的先天性周围血管疾患,具有典型的三联征:毛细血管畸形(葡萄酒色斑)、肢体过度生长、非典型性外侧浅静脉曲张。这种复杂的血管病变是一种混合性血管畸形,有突出的毛细血管、静脉和淋巴管,而没有显著的动-静脉分流。最常累及下肢。影像学检查需要确定静脉病变的范围及深静脉的回流情况。压迫治疗是保守治疗的主要方法。手术包括浅静脉的剥脱、激光治疗等,须根据病人病情指定多学科参与的治疗方案。
Klippel-Trenaunay syndrome (Klippel-Trenaunay syndrome, KTS) is a rare congenital peripheral vascular disease with typical triads: capillary anomalies (wine stains), limb overgrowth, and atypical lateral varicose veins. This complex vascular disease is a mixed vascular malformation with prominent capillaries, veins and lymphatic vessels without significant arteriovenous shunts. The most common involvement of lower limbs. Imaging studies need to determine the extent of venous lesions and deep venous reflux. Oppression is the mainstay of conservative treatment. Surgery, including the exfoliation of superficial veins, laser treatment, etc., according to the patient’s condition designated multidisciplinary treatment programs.