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上皮样血管内皮瘤(EH)1982年首见报道。该病极少见,原发于颅内者更少,迄今仅报道过4例,其中2例为儿童。作者报告1例成年EH病人的治疗过程。 男性,27岁,因右颞部搏动性疼痛、右耳鸣入院。体检:右颞肿胀、压痛,无神经系统阳性体征。头颅平片示右颞骨破坏。CT扫描示右颞部脑外占位,强化明显,颞骨、蝶骨及颞肌受侵。血管造影见血管样新生物由颈外动脉的脑膜中动脉和颞深、颞浅动脉等4支明显增粗的动脉供血。第1次手术因瘤体表面大量出血而中止手术。后进行血管内栓塞,除保留颌内动脉及其远端侧支外,其余肿瘤血管完全阻断。CT检查,栓塞胶散布于瘤内而未溢出瘤体和血管外,瘤体大小如
Epithelioid hemangioendothelioma (EH) first reported in 1982. The disease is rare, with fewer cases of primary intracranial disease, to date, only four have been reported, two of which are children. The authors report the course of treatment in 1 adult EH patient. Male, 27 years old, due to right temporal pulsatile pain, right tinnitus hospitalized. Physical examination: right temporal swelling, tenderness, no signs of nervous system. Skull plain film shows right temporal bone destruction. CT scan showed right temporal brain mass, enhanced obviously, temporal bone, sphenoid bone and temporal muscle invasion. Angiography angiogenic new organisms from the external carotid artery in the middle meningeal and temporal deep, superficial temporal artery 4 significantly thicker arteries. The first operation due to a large number of bleeding on the surface of the tumor stopped surgery. After endovascular embolization, in addition to preserving the distal collateral artery and the lateral branches, the rest of the tumor blood vessels completely blocked. CT examination, embolization glue scattered in the tumor without overflowing the tumor and blood vessels, tumor size as