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皮肤粘膜色素沉着伴胃肠道多发性息肉为本综合征特点。它是一个家族遗传性疾病。由于多发息肉,易引起消化道出血、腹痛,也可导致肠套叠、肠梗阻等一系列症状而就诊。我院发现一例患者,报告如下: 患者,女,22岁。经常腹胀、腹痛,近来解黑色大便三次,有时便鲜血,伴头昏、眼花、乏力。并昏倒一次而入院。 幼年起有口部粘膜紫点,逐渐增大呈斑片状。
Skin mucosal pigmentation with gastrointestinal polyp characteristics of this syndrome. It is a familial hereditary disease. Due to multiple polyps, easy to cause gastrointestinal bleeding, abdominal pain, can also lead to intussusception, intestinal obstruction and a series of symptoms and treatment. A case of patients found in our hospital, the report is as follows: Patients, female, 22 years old. Often abdominal distension, abdominal pain, the recent solution to black stool three times, sometimes blood, with dizziness, vertigo, weakness. And collapsed and admitted to hospital. Juvenile mucosa since the purple point, and gradually increased patchy.