Marfan综合征 (Marfansyndrome,MFS)是一种常染色体显性遗传的全身性结缔组织疾病 ,发病率为 0 0 2 %～ 0 0 3%。主要表现为眼、骨骼和心血管系统畸形。患者身材高、体瘦、两臂伸长的长度大于身高 ,手指细长 ,故称蜘蛛脚样指。眼的表现常有高度近视 ,晶状体脱位。心血管系统 Marfan syndrome (MFS) is an autosomal dominant systemic connective tissue disease with a prevalence of 0 0 2% ~ 0 0 3%. Mainly manifested as eye, bone and cardiovascular deformities. Patients tall, thin, arms length greater than the length of the fingers slender, so that the spider feet like fingers. Eye performance often high myopia, lens dislocation. Cardiovascular System