抗中性粒细胞胞浆抗体(ANCA)相关小血管炎主要指韦格纳肉芽肿瘤(Wegner’s granulomatosi,WG)、显微镜下型多血管炎(Microscopic polyangiitis,MPA)和局灶节段坏死性肾小球肾炎(FSNGN)。该病为自身免疫性疾病,可累及全身多个脏器,肺受累可以表现为肺部阴影、结节和空洞,与肿瘤、肺结核等不易鉴别,肺大出血可危及患者生命。肾受累则多表现为局灶节段坏死性肾小球肾炎和新月体性肾 Anti-neutrophil cytoplasmic antibodies (ANCA) associated vasculitis mainly refers to Wegner’s granulomatosi (WG), Microscopic polyangiitis (MPA) and focal segmental necrosis of the kidney Ball nephritis (FSNGN). The disease is an autoimmune disease that can affect multiple organs of the body. Lung involvement can manifest as lung shadow, nodules and voids, which can not be easily distinguished from tumors and tuberculosis. Bleeding of the lung can endanger the life of the patient. Renal involvement is manifested as focal segmental necrotic glomerulonephritis and crescentic kidney