论文部分内容阅读
报告1例ALK-1蛋白阳性的原发性皮肤CD30+间变性大细胞淋巴瘤。患儿女,6岁。因左下眼睑包块5个月就诊。入院检查见左下眼睑一2.5cm×3.0cm×0.5cm红色包块,组织病理学检查示真皮内大片大细胞浸润,细胞核呈间变性;免疫组化染色示UCHL-1(+)、CD30(+)、ALK-1(+),EBER原位杂交为阴性。ALK蛋白表达模式为细胞质与细胞核。回顾相关文献,该例原发性皮肤CD30+间变性大细胞淋巴瘤检测到ALK蛋白阳性表达系国内首例报告。
One case of primary skin CD30+ anaplastic large cell lymphoma with ALK-1 protein was reported. The child is 6 years old. Due to left lower eyelid mass for 5 months. In the hospital examination, a 2.5cm×3.0cm×0.5cm red mass was seen in the left lower eyelid. Histopathological examination showed large infiltrates in the dermis and nucleus degeneration. Immunohistochemical staining showed UCHL-1(+) and CD30(+). ), ALK-1 (+), EBER in situ hybridization was negative. The ALK protein expression pattern is cytoplasm and nucleus. Recalling the relevant literature, the case of the first case of ALK protein positive expression was detected in this case of primary skin CD30+ anaplastic large cell lymphoma.