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川崎病又称皮肤粘膜淋巴结综合征,是一种以全身血管炎为主要病理改变的急性发热性出疹性小儿疾病。其自限性强。病因尚不明了,临床表现多样,某些特殊体征出现较晚,缺乏特殊的辅助检查而易误诊及漏诊。本院1例误为“咽峡炎,败血症?”现报告如下、患儿,女,3岁。因高热、双膝关节痛8天,四肢、颜面浮肿4天入院。发病后第5天出现一过性大小不一的红色斑丘疹。先后给予鱼腥草注射液、先锋霉素Ⅳ及退热药治疗,病情未见好转。体查:T39.8℃,BP12.0/8.0kPa,右颌下淋巴结肿大,双结膜充血,草梅舌,咽红,右扁桃体Ⅱ度肿大。心肺未见异常。腹部无阳性征。手掌、脚掌皮硬呈朱砂色。实验室检查:WBC20.2×10~9/L,N0.7,L0.3。
Kawasaki disease, also known as mucocutaneous lymph node syndrome, is a type of systemic vasculitis as the main pathological changes in acute febrile children with rash disease. Its self-limiting and strong. Etiology is not yet clear, the clinical manifestations of various special signs appeared later, the lack of special auxiliary examination and misdiagnosis and missed diagnosis. 1 patient was mistaken for “angina, septicemia?” The report is as follows, children, women, 3 years old. Due to high fever, knee pain for 8 days, limbs, face edema admitted to hospital for 4 days. On the fifth day after the onset of a transient red rash of varying sizes. Has given Houttuynia injection, Pioneer ADM Ⅳ and antipyretics treatment, the condition did not improve. Physical examination: T39.8 ℃, BP12.0 / 8.0kPa, submandibular lymph nodes, conjunctival congestion, grass mei ling, throat red, right tonsil Ⅱ degree enlargement. Heart and lung no abnormalities. Abdominal positive sign. Palm, palm leather was vermilion. Laboratory tests: WBC20.2 × 10 ~ 9 / L, N0.7, L0.3.