论文部分内容阅读
目的探讨黏液炎症性纤维母细胞肉瘤(MIFS)的病理特征及鉴别诊断。方法对1例黏液炎症性纤维母细胞肉瘤进行病理学观察并文献复习。结果肿瘤最明显的特征是:有明显异型的肥胖的梭形细胞、神经节细胞样细胞、畸形的RS样细胞或病毒样细胞,还可见到脂母细胞样细胞。免疫组化示肿瘤细胞Vimentin和SMA阳性。结论 MIFS是一种罕见的低度恶性的纤维母细胞肉瘤,易被误诊为良性病变,熟悉其形态学特点有助于诊断和鉴别诊断。
Objective To investigate the pathological features and differential diagnosis of mucinous inflammatory fibroblastic sarcoma (MIFS). Methods A case of mucinous inflammatory fibroblastic sarcoma was observed and reviewed. Results The most obvious features of the tumor were obesity spindle cells, ganglion cell-like cells, degenerative RS-like cells or virus-like cells, as well as adipocyte-like cells. Immunohistochemistry showed that the tumor cells Vimentin and SMA positive. Conclusions MIFS is a rare low grade malignant fibroblastic sarcoma, easily misdiagnosed as benign lesions, familiar with its morphological characteristics contribute to the diagnosis and differential diagnosis.