颅咽管瘤为一常见的先天性颅内肿瘤,在小儿非胶质瘤中居首位,据国内外文献报告,其发病率占小儿全部颅内肿瘤的9～17.4%;在成人其发病率则为1.7～4.6%。一般认为,颅咽管瘤来自胚胎期颅颊裂残留的鳞状上皮细胞,虽具有良性组织学特征,但其临床过程却呈恶性。这不仅由于颅咽管瘤起病 Craniopharyngioma is a common congenital intracranial tumor, which ranks first in pediatric non-glioma. According to the domestic and international literature, the incidence of craniopharyngiomas accounts for 9% to 17.4% of the total intracranial tumors in children. In adults, the incidence is 1.7 ~ 4.6%. Generally believed that craniopharyngioma from the embryonic cranial cheek cleft residual squamous epithelial cells, although with benign histological features, but its clinical course was malignant. This is not only due to the onset of craniopharyngiomas