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孤立肾同时伴有旋转不良和输尿管高位狭窄临床极为少见。我院发现1例,现简要报告如下。 患者,男性,10岁,因腹痛血尿8天入院,既往有类似发作史3年,体检发育正常,双眼睑略浮。血压、血常规、尿素氮均正常。尿常规蛋白(+),红细胞(++)。B超检查:左肾区未探及左肾,未见左输尿管喷尿。右肾各径偏大。下极上抬,偏横位。右肾门转向腹内侧,肾盂内4~5枚强光团,直径1.0~1.5cm伴声影。右肾集合系统分离,暗区达1.8cm,右输尿管上段与肾门相接处,管腔显示不清,右输尿管中、下段显示清晰,内腔0.5~0.7cm,末端入膀胱处喷尿正常。B超诊断;左肾缺如,右肾发育不良,右肾多发性结石伴积水。静脉肾盂造影报:左肾缺如,右肾旋转不良,多发性结石,右输尿管高位狭窄。手术术所见:右肾
Isolated kidneys accompanied by malaise and high ureteral stenosis are extremely rare. 1 case found in our hospital, is now briefly reported as follows. Patients, men, 10 years old, admitted to hospital for abdominal pain and hematuria for 8 days, had a history of similar attacks for 3 years, normal physical examination, slightly eyelid eyelid. Blood pressure, blood, urea nitrogen were normal. Urine protein (+), red blood cells (++). B-ultrasound: left kidney area is not explored and left kidney, no left ureter was found. Right kidney diameter larger. Under the pole lift, partial horizontal position. Right kidney door turned to the ventral, renal pelvis within 4 to 5 bright light group, diameter 1.0 ~ 1.5cm with sound shadow. Right renal collecting system separation, the dark area of up to 1.8cm, the upper right ureter and renal access phase, the lumen is not clear, the right ureter, the lower segment showed a clear lumen 0.5 ~ 0.7cm, the end of the urinary bladder at normal urination . B-ultrasound; absence of left kidney, right kidney dysplasia, multiple stones of the right kidney with water. Intravenous pyelography: the absence of left kidney, right renal malrotation, multiple stones, high right ureteral stricture. Surgical findings: the right kidney