区域性门静脉高压症(regional portal hypertension,RPH)临床上不多见,属于肝外型门静脉高压症的特殊类型,约占肝外型门静脉高压症的5%[1]。1954年Leger首先描述本症,20世纪60年代Turrill提出左侧肝外型门静脉高压症的概念,后来对其的研究大部分集中在慢性胰腺炎引起的孤立性脾静脉血 Regional portal hypertension (regional portal hypertension, RPH) is rare in clinical practice, is a special type of extrahepatic portal hypertension, accounting for about 5% of extrahepatic portal hypertension [1]. 1954 Leger first described the disease, the 20th century, 60 Turrill proposed the concept of left hepatic portal hypertension, and later most of its research focused on chronic pancreatitis caused by isolated splenic venous blood