特发性间质性肺炎(idiopathic interstitial pneu-monia,IIP)又名特发性肺纤维化,为一组原因不明的进行性下呼吸道疾病,病理过程一般为进展缓慢的弥漫性肺泡炎和(或)肺泡结构紊乱,最终导致肺泡结构破坏,形成肺泡腔内完全型纤维化和囊泡状的蜂窝肺。然而,对IIP概念的理解一直存? Idiopathic interstitial pneu-monia (idiopathic interstitial pneu-monia, also known as idiopathic pulmonary fibrosis, a group of unexplained progressive lower respiratory tract disease, the pathological process is generally slow progress of diffuse alveolitis and ( Or) Alveolar structural disorder, eventually leading to the destruction of alveolar structure, the formation of alveolar cavity complete fibrosis and vesicular honeycomb lung. However, the concept of IIP has been stored?