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肺泡微结石症(Pulmonary alveotarmicrolithiasis)多认为系遗传性疾病,常染色体单纯劣性遗传,约55%以上发生在同胞或近亲中。目前国内报告仅余10例。现将我院一例,报告于下。患者女,72岁,农民。自述近4~5年来间有咳嗽,活动后气促,但仍可做轻微田间劳动和一般家务。入院前8个月开始咳嗽,气短加重,伴紫绀。却无发热、盗汗。否认有夜间阵发性呼吸困难、尿少、浮肿史。既往无结核病和粉尘接触史。当即以慢性支气管炎、合并感染、肺心病
Pulmonary alveolar microlithiasis (Pulmonary alveotarmicrolithiasis) and more that Department of hereditary diseases, autosomal poor genetic, about 55% occurred in siblings or close relatives. The current domestic report only 10 cases. Now a case of our hospital, the report below. Female patient, 72 years old, farmer. Almost 4 to 5 years since the statement of cough, shortness of breath after the event, but still do minor field work and general housework. 8 months before admission cough, shortness of breath, with cyanosis. No fever, night sweats. Denied nocturnal paroxysmal dyspnea, oliguria, history of edema. Past history of TB and dust exposure. Immediately to chronic bronchitis, co-infection, pulmonary heart disease