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目的 探讨椎基底动脉延长扩张症(vertebrobasilar dolichoectasia,VBD)的临床表现及诊断方法.方法 回顾2例典型椎基底动脉延长扩张症患者临床及影像学资料,并结合文献进行分析.结果 VBD具有时间顺序占位效应,面肌痉挛、低钾、三叉神经痛、眩晕发作、肢体偏瘫相继发生,VBD具有进展性.结论 VBD症状多样,具有时间顺序,面肌痉挛可能是较早出现的症状.部分后循环缺血(posterior circulation ischemia,PCI)症状可能仅仪是VBD脑干压迫的结果 ,而不是传统意义上的PCI.“,”Objective To explore the clinical presentation and diagnosis of vertebrobasilar dolichoectasia (VBD) presented with brainstem compression symptoms. Methods Clinical and imaging data of 2 typical cases of Vertebrobasilar dolichoectasia were retrospectively analyzed and relevant literature was reviewed. Results Hemifaeialspasm, hypokalemic paralysis, trigeminal neuralgia, vertigo, hemiplegia progressively occurred in a chronological order due to the extension of VBD. Conclusions VBD can cause to a variety of symptoms in a chronological order and early hemifaeialspasm may be a hint for early diagnosis of VBD. Posterior circulation ischemia (PCI) may result from VBD.