外耳道外生骨疣伴先天性胆脂瘤临床罕见。1994年6月，我们在为一外耳道巨大外生骨疣手术时发现同时伴有先天性颞骨内胆脂瘤。现报告如下。患者，男，26岁。因右外耳道肿物进行性增大伴有听力下降3年，于1994年6月5日入院，肿物初起如黄豆大，无红肿及疼痛，近半年逐渐增大，填 External auditory meatus genital warts with congenital cholesteatoma rare clinical. In June 1994, we found a congenital temporal bone cholesteatoma at the same time as a huge external excretion of external genital warts surgery. The report is as follows. Patient, male, 26 years old. Because of the right external auditory meatus progressive enlargement accompanied by hearing loss for 3 years, was admitted on June 5, 1994, the beginning of the tumor such as soybeans, no swelling and pain, gradually increased in the past six months, fill