横纹肌肉瘤占软组织肉瘤的15～20％,在软组织肉瘤中居第3位。近年来,报告例数不断增加。异位横纹肌肉瘤比横纹肌组织本身所发生者远为多见。据不同作者报告,这些部位的横纹肌肉瘤,在文献上累积的例数分别如下。鼻咽部96例,喉部9例,中耳88例,副鼻窦部11例,前列腺60余例,精索54例,肾脏8例,肛周及直肠周部11例,胆道25例,原发性肺横纹肌肉瘤12例,原发性颅内横纹肌肉瘤10 Rhabdomyosarcoma accounts for 15 to 20% of soft tissue sarcoma and ranks third in soft tissue sarcoma. In recent years, the number of reports has continued to increase. Ectopic rhabdomyosarcoma is far more common than the striated muscle itself. According to reports by different authors, the number of cases of rhabdomyosarcoma in these sites that have accumulated in the literature are as follows. There were 96 cases of nasopharynx, 9 cases of larynx, 88 cases of middle ear, 11 cases of paranasal sinus, more than 60 cases of prostate, 54 cases of spermatic cord, 8 cases of kidney, 11 cases of perianal and rectal circumference, and 25 cases of biliary tract. 12 cases of primary pulmonary rhabdomyosarcoma, primary intracranial rhabdomyosarcoma 10