定义:是以无(少)汗、少毛、牙先天缺失(或发育不全)三大症状为主,伴其他外胚叶组织发育不良的先天性异常。症状:皮肤一般较薄,干燥、发白,手掌、足底部多可见角化症,面部常出现湿疹样丘疹。上脸起皱。由于小汗腺发育不全或缺失,排汗障碍,容易导致高热。鼻腔、口腔粘液腺缺乏,有时发生萎缩性鼻炎。成年后可长出胡 Definition: There is no (less) sweat, less hair, tooth defects (or hypoplasia) three main symptoms, with other ectodermal dysplasia congenital anomalies. Symptoms: the skin is generally thin, dry, pale, palms, feet and more visible keratosis, often appear eczema-like papules on the face. Wrinkled on the face. Due to hypokalemia hypoplasia or absence of perspiration, easily lead to high fever. Nasal, oral mucous gland deficiency, and sometimes atrophic rhinitis. Adult grows Hu