1名54岁右利手的妇女于1992年6月出现2次抽搐。脑CT及脑脊液检查正常。几周后病人颈项强直,头痛,恶心,呕吐,眩晕,定向障碍,昏睡。神经学检查示右侧第三颅神经麻痹,左侧偏瘫,MRI检查后右大脑中动脉急性脑梗塞,掩盖了右侧沟中的肿块。脑血管造影示右大脑中动脉几乎完全闭塞,而在后循环区域有多灶性(“串珠样”)狭窄。有关血管炎和感染的多项脑脊液和血清检查均为阴性,脑脊液细胞学检查未 A 54-year-old right-handed woman had two convulsions in June 1992. Brain CT and cerebrospinal fluid were normal. A few weeks later the patient had stiff neck, headache, nausea, vomiting, dizziness, disorientation and lethargy. Neurological examination showed the right cranial nerve paralysis on the right, left hemiplegia, MRI right cerebral artery after acute cerebral infarction, to cover the right side of the tumor in the groove. Cerebral angiography showed almost complete occlusion of the right middle cerebral artery and multifocal (“beaded”) stenosis in the posterior circulation area. A number of cerebrospinal fluid and serum tests on vasculitis and infection were negative, CSF cytology was not detected