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腹膜假性粘液瘤是一种临床上罕见的疾病,其特征是腹内有大量的粘蛋白聚集.大多数来源于阑尾或卵巢癌,亦有见于胰腺癌.乳癌和胆管癌的报告.本病多属于低度恶性的癌肿.大多数病人发生腹膜弥漫性播散.远处转移则不多见.目前所倡导的最佳的病人治疗方案包括:手术清除腹内粘蛋白、放疗(放射性核素腹内滴注和外照射)和化疗(腹腔内化疗和全身化疗).由于所研究的病种的差异,病例例数小和本病病程长等原因,使对各种治疗结果的评价较为困难.
Peritoneal pseudomyxoma is a clinically rare disease characterized by a large amount of mucin aggregation in the abdomen. Most of them are from appendix or ovarian cancer, but also from pancreatic cancer, breast cancer and cholangiocarcinoma. Mostly belong to low-grade cancer. Most patients have peritoneal diffuse dissemination. Distant metastasis is rare. Currently the best patient treatment options advocated include: surgical removal of intramuscular mucin, radiotherapy (radioactive nucleus Intra-abdominal instillation and external irradiation) and chemotherapy (intraperitoneal chemotherapy and systemic chemotherapy). Due to the differences in the types of diseases studied, the small number of cases and the length of the disease, etc. difficult.