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原发性直立性低血压,又称为 Shy-Draget 综合征,是一种少见的神经系统多系统性疾病,病因不明,易于误诊。现将我们从1977年以来收治的6例报告如下。临床资料本组6例均为男性,年龄43—57岁,发病年龄42—53岁。首发症状:头晕、晕厥、走路不稳4例、尿频、阳萎2例。体征:本组6例均有表情呆板,构音不清,双手震颤,水平眼震和共济失调。6例有5例引出病理反射,肌张力增高。血压:6例测量坐位血压均较卧位降低40~60/30~40mmHg。头颅 X 光平片及颈椎片均正常。脑电图1例不正常。心电图1例窦性心动过缓伴心律不
Primary orthostatic hypotension, also known as Shy-Draget syndrome, is a rare, multisystem neurological disease with unknown etiology and misdiagnosis. We now report 6 cases admitted since 1977 as follows. Clinical data The group of 6 patients were male, aged 43-57 years, the age of onset 42-53 years old. First symptom: dizziness, syncope, walking instability in 4 cases, frequent urination, impotence in 2 cases. Signs: This group of 6 patients had dull facial expressions, unclear articulation, tremor hands, level nystagmus and ataxia. Five of the six cases elicited pathological reflexes and increased muscle tone. Blood pressure: 6 cases measured sitting blood pressure lower than the lying position 40 ~ 60/30 ~ 40mmHg. Skull X-ray films and cervical films were normal. EEG 1 case is not normal. One case of electrocardiogram sinus bradycardia with arrhythmia