颅咽管瘤系颅内先天性肿瘤,亦称拉克氏(Rathke)囊肿、鞍上囊肿、垂体蒂瘤等。肿瘤来自胚胎发育过程中颅咽管残存的鳞状上皮细胞,这些细胞多在垂体蒂部出现,故肿瘤多发生于鞍上,亦可发生于胎生期颅咽管曾经存在过的任一部位。有关颅咽管瘤发病率的报道不一:刘德华(1)报道占颅内肿瘤的7.8％,赵以成(2)为3.5％。我院自1973年5月至1980年7月共收治42例,均经手术与病理检查证实,占同时期 Craniopharyngiomas Department of intracranial congenital tumors, also known as Rakke (Rathke) cysts, suprasellar pituitary pedicle, and so on. The tumor comes from the squamous epithelial cells remaining in the craniopharyngiomas during embryonic development. Most of these cells appear in the pedicle of the pituitary gland. Therefore, the tumor mostly occurs in the saddle and may occur in any part of the craniopharyngioma that has existed during the fetal life. The incidence of craniopharyngioma varies according to coverage: Andy Lau (1) reported 7.8% of intracranial tumors and Zhao Yicheng (2) 3.5%. Our hospital from May 1973 to July 1980 were treated 42 cases were confirmed by surgery and pathology, accounting for the same period