报告了10例原发性肾小管性酸中毒患儿4～10年随访结果.死亡2例,自然痊愈1例.7例仍在接受治疗,其中3例治疗4年至5年2个月后身高达正常水平,除轻度骨骼畸形外无其他异常发现;4例随访4年到7年3个月身高仍未正常,可见不同程度骨骼畸形,定期复查血化学3例仍存在轻度酸中毒. Reported 10 cases of primary renal tubular acidosis in children 4 to 10 years follow-up results, 2 patients died of natural recovery in 1 case, 7 patients were still under treatment, of which 3 were treated 4 years to 5 years after 2 months Up to the normal level, with no exception except mild skeletal deformity; 4 cases were followed up for 4 to 7 years 3 months height is not normal, showing varying degrees of skeletal deformity, regular review of 3 cases of blood chemistry there are still mild acidosis .