乳房外Paget病（ExtramammaryPasetDisease）是指位于乳房以外的，临床和组织学表现都类似于乳房Paget病的一种恶性肿瘤，临床罕见。本文报告肛周Paget病1例，并结合文献讨论。病例患者女性70岁，主因肛门疫痒、肛门肿物3年，加重4个月，于95年12月入院。3年前无诱因出现肛周痒 Extramammary Paset Disease refers to a type of malignant tumor that is located outside the breast and is clinically and histologically similar to breast Paget disease and is rare in clinical settings. This article reports one case of perianal Paget disease, and discusses the literature. The case patient was 70 years old and she was admitted to the hospital in December 1995 due to an anal fistula and anal mass for 3 years. He was aggravated for 4 months. Three years ago, there was no cause of anal itch