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肝豆状核变性又称Wilson氏病,临床上并不少见,但对该病的脑诱发电位(BE-Ps)的观察,国内外报道的均不多,作者曾对5例患者作过初步报道,以后又积累了一些病例,现将16例的BEPs报告如下。资料和方法 16例中除1例为门诊病例外,均为住院患者,有2例为再次住院。男11、女5,年龄9~32岁。既往有肝病史3例,肾炎史1例,2例曾行脾切除术。家族中兄弟姐妹有同样病患者6例,有肝病患者4例。发病至住院期间5个月至10年,以1~2年者为多。症状及体
Hepatolenticular degeneration, also known as Wilson’s disease, is not uncommon clinically, but the observation of the brain evoked potential (BE-Ps) of the disease, not many reports at home and abroad, the author had 5 patients had a preliminary Reported, and later accumulated some cases, now 16 cases of BEPs report as follows. Materials and Methods All but one of the 16 patients were hospitalized, and two were hospitalized again. Male 11, female 5, aged 9 to 32 years old. Past history of liver disease in 3 cases, history of nephritis in 1 case, 2 cases had splenectomy. Family brothers and sisters have the same disease in 6 cases, 4 cases of liver disease. Incidence of hospitalization from 5 months to 10 years, 1 to 2 years were more. Symptoms and body