眼瘢痕性类天疱疮系一种罕见的慢性进行性疾病,过去在命名方面颇为混乱,曾称为良性粘膜类天疱疮、瘢痕性类天疱疮、眼天疱疮、结膜天疱疮及特发性结膜皱缩等。迄今已大致统一称为眼瘢痕性类天疱疮。 Thost(1911)曾根据临床征象将该病与其他类型的天疱疮加以区分;Lever(1951)又根据临床征象与组织病理学所见将类天疱疮与天疱疮进 Eye Cicatricial Pemphigus is a rare and chronic progressive disease that used to be quite confusing in nomenclature and has been described as benign mucocutaneous pemphigoid, cicatricial pemphigoid, ocular pemphigoid, conjunctival pericardium Sores and idiopathic conjunctival folds and so on. So far has been generally known as eye cicatricial pemphigoid. Thost (1911) distinguished the disease from other types of pemphigus based on clinical signs; Lever (1951), in turn, classified both pemphigoid and pemphigus according to clinical signs and histopathology