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本病简称红细胞G6PD缺陷症,临床主要包括蚕豆病、药物性溶血性贫血、新生儿G6PD缺陷溶血症和遗传性非球形红细胞溶血性贫血Ⅰ型,以前两者为多见。本病为遗传病,属性连锁不完全显性遗传,男性发病率明显地高于女性,男女发病率之比约为7～14:1。本病在地理上的分布极广,全世界人口中约1亿人有红细胞G6PD的缺陷。在我国以四川、广东、广西、福建等省区发病率高。广东某地群体普查发现
The disease referred to as erythrocyte G6PD deficiency, clinical mainly including broad bean disease, drug hemolytic anemia, neonatal G6PD deficiency hemolytic disease and hereditary non-spherical hemolytic anemia type I, the former two are more common. The disease is genetic disease, property chain incomplete dominant inheritance, the incidence of men was significantly higher than that of women, the incidence of men and women is about 7 ~ 14: 1. The disease is widely distributed in geography, about 100 million people worldwide have the defects of erythrocyte G6PD. In our country, Sichuan, Guangdong, Guangxi, Fujian and other provinces have a high incidence. Census of a certain area in Guangdong found