视网膜色素变性从幼小儿童期起出现夜盲和视野狭窄,逐渐进行,到中年或老年而失明,其原因不明。病理学特征:视细胞层有选择性的消失和色素上皮细胞的增殖,特别是初期即可看到视杆细胞的变性。哺乳动物视杆细胞内有强有力的抗原,可诱发色素膜炎,特别是可溶性的视网膜S抗原对脏器有特异性,可引起体液免疫和细胞免疫 Retinitis pigmentosa has been characterized by night blindness and narrowing of the visual field from early childhood, which is progressing to blindness in middle age or old age, for unknown reasons. Pathological features: depending on the selective loss of the cell layer and the proliferation of pigment epithelial cells, especially in the early phase of the degeneration of rod cells. Mammalian rod cells have a strong antigen, can induce uveitis, especially the soluble retinal S antigen specific organ, can cause humoral and cellular immunity