原发性鼻腔恶性黑色素瘤较少见。本文报告7例,占本院收治身体恶性黑色素瘤的17.5%,为耳鼻喉科恶性肿瘤的1.46%。主要症状为鼻出血,原发在鼻腔多见,累及鼻窦少。恶性度高,易复发,预后极差。本组存活最长4年半,最短术后4个月死亡。2例术后4个月复发,1例死于肺转移。治疗以手术为主,病变位于鼻腔者取鼻侧切开术,累及鼻咽部者以腭间径路术式为宜。本文结合文献讨论病因病理等有关问题。 Primary nasal malignant melanoma is less common. This article reports 7 cases, which accounted for 17.5% of the malignant melanomas treated in our hospital and 1.46% of otolaryngologic malignancies. The main symptom is nosebleeds, which is more common in the nasal cavity and less in the sinuses. High degree of malignancy, easy to relapse, and poor prognosis. The group survived for a maximum of 4 and a half years, and the shortest postoperative 4 months died. Two cases relapsed 4 months after surgery and one died of lung metastasis. The treatment was mainly surgery, and the lesion was located in the nasal cavity and the nasal incision was taken. Those who were involved in the nasopharyngeal were suitable for the intercondylar pathway. This article combines the literature to discuss the etiology and pathology and other related issues.