人工电子耳蜗植入术在近年来有了很快的发展,以前内耳尤其是耳蜗畸形被视为手术的禁忌证,最近国外学者报道了耳蜗畸形的人工耳蜗植入术,而且效果与正常耳蜗结构者相似[1],但这种手术的风险很高,需要影像学详细评价内耳的结构,听觉传导通路以及听觉中枢的功能。迷路缺失、耳蜗未 Artificial cochlear implant has been developing rapidly in recent years. Previously, the inner ear, especially cochlear deformity, was considered a contraindication for surgery. Recently, foreign scholars reported cochlear cochlear implant cochlear deformity, and the effect with the normal cochlear structure Are similar [1], but the risk of such surgery is high and requires imaging to evaluate in detail the structure of the inner ear, auditory conduction pathways, and the function of the auditory center. Lost lost, cochlear is not