本病是小儿的一种特殊神经疾患,其病因和发病机理尚未明了。临床特点为急性起病,有发热、惊厥及意识障碍。病情进展迅速,常在昏迷后1～3日内死亡,存活者常遗留运动及智力障碍。病理特点为急性脑肿胀及内脏(主要是肝脏)脂肪变性。此病于1963年首先由Reye 等报告。关于本病的命名,有人称为婴儿急性特发性脑病、原因不明的急性脑病、小 The disease is a special neurological disorders in children, its etiology and pathogenesis is not yet clear. Clinical features of acute onset, fever, convulsions and disturbance of consciousness. Rapid progression of the disease, often in coma after 1 to 3 days of death, survivors often left behind movement and mental retardation. Pathological features of acute brain swelling and visceral (mainly liver) steatosis. This disease was first reported by Reye et al in 1963. On the naming of this disease, some people called the baby acute idiopathic encephalopathy, unexplained acute encephalopathy, small