遗传性出血性毛细血管扩张症少见 ,鼻出血是该病最常见和严重的并发症 ,而且常常表现为顽固性鼻出血 ,临床治疗非常棘手。我们遇见 1例 ,现报道如下 :患者　女 ,5 1岁。因反复发作鼻出血 2 0年、加重 7ｄ入院。鼻出血无明显诱因 ,双侧鼻腔交替出血 ,反复发作 ,出血量最多达 5 0 Hereditary hemorrhagic telangiectasia rare, epistaxis is the most common and serious complications of the disease, and often manifested as intractable epistaxis, clinical treatment is very difficult. We met one case, are now reported as follows: Female patients, 5 1 years old. Due to recurrent nasal bleeding 20 years, increased 7d admission. No obvious cause of epistaxis, bilateral nasal alternating hemorrhage, recurrent, bleeding up to 50