肝豆状核变性（bepatdentic－ulardegeneration）即Wilson病（WD），是一种常染色体隐性遗传性疾病，以铜代谢障碍为其特征。虽然该病可终生治疗，但临床表现复杂多样，往往易被误诊为其它疾病，以致延误治疗，甚至危及生命。现将我院儿科1985～1997年12年间收治的28例患儿误诊 Bepatdentic-ulardegeneration, Wilson’s disease (WD), is an autosomal recessive disorder characterized by copper metabolic disorders. Although the disease can be treated for life, the clinical manifestations are complex and diverse and are often easily misdiagnosed as other diseases, resulting in delays in treatment and even life-threatening. Now my hospital pediatric from 1985 to 1997 12 years admitted to 28 cases of misdiagnosed children