Fahr病最初由Fahr于1930年提出，为家族遗传性疾病，也可见散发病例，临床主要表现为智能障碍，锥体束征，锥体外系症状及小脑症状，也可见癫痫发作，CT示纹状体，苍白球及齿状核钙化，病理上表现为脑小血管钙化而无动脉硬化，故又称特发性纹状体苍白球齿状核钙化或非动脉硬化 Fahr disease was originally proposed by Fahr in 1930. It is also a familial hereditary disease with sporadic cases. The main clinical manifestations are mental retardation, pyramidal tract signs, extrapyramidal symptoms and cerebellar symptoms, as well as seizures, CT streaks Body, globus pallidus and dentate nuclei calcification, pathological manifestations of cerebral small vessel calcification without atherosclerosis, it is also known as idiopathic striatal pale odontoid calcification or non-arteriosclerosis