肺动脉高压(pulmonary hypertension,PH)是先天性心脏病(先心病)最常见的并发症,它不仅影响外科治疗的效果,还会增加麻醉的危险,是围手术期死亡的常见原因。先心病合并PH的患儿心肌受累,心肌应激性增加,心肌收缩力和储备功能明显下降,对麻醉和手术的耐受性差。本院自2009年6月 Pulmonary hypertension (PH) is the most common complication of congenital heart disease (congenital heart disease), which not only affects the effect of surgical treatment but also increases the risk of anesthesia and is a common cause of perioperative death. Patients with congenital heart disease complicated with PH myocardial involvement, increased myocardial stress, myocardial contractility and reserve decreased significantly, poor tolerance to anesthesia and surgery. Our hospital since June 2009