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本文的主要目的是用“残疾”和“生活质量”来评价肌营养不良(MD)的影响,同时评价了适合于MD测量仪器的效度和信度。 资料与方法 在神经肌肉疾病的人口普查中,57名年龄16～64岁患者诊断有32名肌强直性疾患(myotonic disorder)(其中肌强直性营养不良30例,先天性肌强直2例),8名迟发性遗传性远端肌病(MDTH),另17名为其它原发性MD,本文称之为“其它MD型”,本研究主要用Brooke肌肉检测法、ADL梯段(在Katz ADL指数基础上制定)及自报
The main purpose of this paper is to evaluate the impact of muscular dystrophy (MD) on “disability” and “quality of life” and evaluate the validity and reliability of MD measuring instruments. Materials and Methods In a population census of neuromuscular diseases, 32 patients with myotonic disorders (30 myotonic dystrophy and 2 congenital myotonia) were diagnosed in patients aged 16-64 years, Eight late-onset hereditary distal myopathies (MDTH) and another 17 are other primary MDs are referred to herein as “other MD types.” In this study, we used the Brooke muscle assay, the ADL bench (in Katz ADL index based on the development) and self-reported