目的探讨外周性原始神经外胚层瘤(pPNET)的影像学表现,以提高对本病的认识。方法搜集暨南大学第四附属医院经病理证实的pPNET 6例,行CT平扫及增强扫描,分析其影像学表现特点。结果 3例病灶位于胸腔,1例位于颈胸部,1例位于髂骨,1例位于大腿。CT显示大部分病例主要表现为边界清的软组织肿块,密度不均匀伴坏死、囊变,极少钙化,增强后明显不均匀强化。发生于骨的PNET CT表现为溶骨性骨质破坏并软组织肿块形成。结论外周性PNET的CT表现缺乏特异性影像学特征;CT检查可显示肿瘤的内部结构,明确肿瘤的范围和发现远处转移。 Objective To investigate the imaging features of peripheral primitive neuroectodermal tumor (pPNET) to improve the understanding of this disease. Methods Six cases of pPNET confirmed by pathology were collected from the Fourth Affiliated Hospital of Jinan University. All patients underwent CT scan and contrast-enhanced scan, and their imaging features were analyzed. Results Three lesions were located in the chest cavity, one in the neck and thorax, one in the ilium and one in the thigh. CT showed most cases of soft tissue mass showed clear border, uneven density with necrosis, cystic degeneration, minimal calcification, enhanced significantly enhanced after heterogeneity. PNET CT occurred in the bone showed osteolytic osteolysis and soft tissue mass formation. Conclusion The CT findings of peripheral PNET lack of specific imaging features; CT examination can show the internal structure of the tumor, clear the scope of the tumor and found distant metastasis.