嗜酸细胞增生性淋巴肉芽肿是一种原因不明的肉芽肿性病。临床上较少见,国内报道56例,均为男性,耳鼻咽喉科文献国内未见报道。国外近年来在耳鼻咽喉科文献中才有报道,但多发生在耳部。本文报告1例女性蝶筛区嗜酸细胞增生性淋巴肉芽肿。患者,女,30岁,头疼5年,右眼失明1年,左眼突出、失明半年,按球后视神经炎、视神经交叉蛛 Eosinophilic lymphogranuloma is an unexplained granulomatous disease. Clinically rare, 56 cases reported in the country, are men, no literature of the Department of Otorhinolaryngology was reported. In recent years, foreign literature has been reported in the Department of Otolaryngology, but occurred in the ear. This article reports a female butterfly sieve eosinophilic lymphogranuloma. Patient, female, 30 years old, headache for 5 years, blindness in right eye for 1 year, left eye prominent, blindness for 6 months, retrobulbar optic neuritis, optic nerve cross spider