新生儿肾上腺髓质先天性微小交感神经母细胞瘤少见,Robbins 认为罕见,国内亦尚少报道,现报告一例。临床资料:本例系妊娠八个半月早产女性婴儿,出生后二天因呼吸,心力衰竭而死亡。病理所见:体重1,700g,身长41cm。双侧肾上腺重3.5g,右侧肾上腺无病变,左侧肾上腺呈月牙形,3×1.5×0.5cm 大,灰黄色,切面皮质与髓质分界较清楚,未见明显肿块。显微镜下:左侧肾上腺髓质中见大片小圆形细胞,类似淋巴细胞,大小形状颇为一致,核染色深,胞浆少,核分裂象多见。瘤 Neonatal adrenal medulla congenital micro-sympathetic neuroblastoma rare, Robbins that rarely seen in China are still less reported, a report is now reported. Clinical data: In this case, eight and a half months of pregnancy, preterm birth of female infants, two days after birth due to respiratory and heart failure and death. Pathology seen: weight 1,700g, length 41cm. Bilateral adrenal weight 3.5g, the right adrenal no lesions, the left adrenal was crescent-shaped, 3 × 1.5 × 0.5cm large, gray yellow, cut the cortical and medullary boundaries more clearly, no significant mass. Microscope: the left adrenal medulla large tracts of small round cells, similar to lymphocytes, the size of the shape is quite consistent, deep staining, less cytoplasm, mitotic more common. tumor