Sturge-weber 综合征临床较少见。其最常见的特征。(1)面部三叉神经分布区葡萄酒色斑;(2)有癫痫发作史;(3)智力减退和智力障碍;(4)眼睛病损常伴“青光眼”(5)头颅正侧位 X 线可见:顶、枕区有钙化。以上症状有2个以上即可确诊。笔者遇到1例典型病例,患有上述特征的全部表现,现报告如下。患者男、16岁。主诉:先天性面部血管痣。智力障碍,反复抽搐10年余。现病史:出生后其家长即发现患者左面部有片状 Sturge-weber syndrome clinical less common. Its most common feature. (1) facial trigeminal nerve distribution of wine stains; (2) history of seizures; (3) mental retardation and mental retardation; (4) eye lesions often accompanied by “glaucoma” (5) : Top, occipital calcification. More than two symptoms can be diagnosed. I encountered a typical case of patients suffering from all the above characteristics of the performance, are as follows. Male patient, 16 years old. Chief Complaint: Congenital facial vascular nevus. Mental retardation, repeated seizures more than 10 years. Current history of illness: after birth, the parents found that there is flake on the left side of the patient