先天性外胚叶发育不良是一组复合性先天疾患。一般分两种类型:少汗型及多汗型。前者又称 Christ—Siemen 综合征①。病例报告毛××,男,56天,因咳呛半月,发热1天入院。在院外体温最高达40℃。第三胎第三产,过期18天顺产,母乳喂养。父母非近亲婚配。家族中无同类病患 Congenital ectodermal dysplasia is a group of complex congenital disorders. Generally divided into two types: less sweat and sweating type. The former also known as Christ-Siemen syndrome ①. Case report hair × ×, male, 56 days, cough for half a month due to cough, fever 1 day admission. Outside the hospital temperature up to 40 ℃. Tertiary third birth, 18 days expired, breastfeeding. Parents non-relatives marriage. No other family members of the disease