横纹肌肉瘤(rhabdomyosarcoma,RMS)为常见的软组织肿瘤之一,年龄40岁以上者罕见,是儿童较常见的恶性肿瘤之一,占儿童癌症第7~8位,也是0~20岁儿童及青少年期软组织肉瘤中最常见的类型,约占50%[1];其发病部位、病理类型与年龄有关[2];而决定其预后的主要因素包括肿瘤部位、病理分 Rhabdomyosarcoma (RMS), one of the common soft tissue tumors, is rare in people over 40 years old. It is one of the most common malignant tumors in children and accounts for 7-8 of children’s cancers. It is also used by children aged 0-20 years and adolescents The most common type of soft tissue sarcoma, accounting for about 50% [1]; its location, pathological type and age [2]; and determine the prognosis of the main factors include the tumor site, pathological points