急性分化性组织细胞增生症,是一种急性进行性、系统性、分化性组织细胞增生性疾病。常见于3岁以内婴幼儿,少数为新生儿。本病的基本病理特点为单核巨噬细胞增生和浸润,累及多个器官和组织,亦可仅侵犯某一器官,预后很差,病儿常在短期死亡。我教研室1964～1980年来共尸检11例,均经病理组织学确诊为网状细胞增生症及 Acute differentiation of histiocytosis, is an acute progressive, systematic, differentiated histiocytosis. Common in infants and children less than 3 years old, a small number of newborns. The basic pathological features of this disease are mononuclear macrophage hyperplasia and infiltration, involving multiple organs and tissues, but also infringe on an organ, the prognosis is poor, sick children often die in the short term. My teaching room from 1964 to 1980, a total of 11 cases of autopsy, were diagnosed by histopathology as reticular cell hyperplasia and