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本病又称Kugelberg—Welander病,是一种特殊类型的运动神经元病。现报告一例。 盛某某,男,33岁,因缓进性肌萎缩约20年于1985年5月20日入院。诉于13岁左右,发现左大腿肌肉变瘦,力弱,走路摇摆。数年后渐现右上臂及同侧胸大肌变薄,提拳力减弱,常感酸困不适,肌肉跳动。近年来对侧肢体亦出现肌肉颤动、酸困痛。病程中曾多方求医,但未能阻止病情进展。患者父母系近亲(姑表)婚配。弟妹九人中,其五弟亦罹
The disease, also known as Kugelberg-Welander disease, is a special type of motor neuron disease. Now report a case. Shing Moumou, male, 33 years old, was admitted to hospital on May 20, 1985 because of progressive amyotrophy for about 20 years. About 13 years old, found that the left thigh muscles become thin, weak, walk swinging. A few years later, the right upper arm and the ipsilateral pectoralis major became thinner and the fist strength was weakened. In recent years, contralateral limb also appeared muscle tremor, acid pain. During his course of treatment, he had many requests for medical treatment, but failed to stop the progression of the disease. Patient parents relatives (Gui table) marriage. Nine siblings, the fifth brother also suffered