论文部分内容阅读
目的 :报告 1例主要以渐进性运动增多和红细胞形态异常改变为特点的临床综合征———舞蹈 棘红细胞增多症。方法 :复习本例临床资料 ,结合近期文献进行分析。结果 :本例的临床表现多种多样 ,以舞蹈运动、自症、抽动症样喉部发声、肌张力障碍、面部运动过多、认知 精神障碍和周围神经损害等神经系统症状表现 ,以及周围血出现棘红细胞增多组成的综合征为特征。结论 :尽管无特效疗法 ,一般认为安坦、溴隐亭、地西泮、氯硝西泮和抗 5 HT剂等均无效 ;但左旋多巴和氟哌啶醇的疗效评价不一。国内报告的 4例中 ,3例 (含本例 )口服氟哌啶醇后舞蹈运动和自症获得近期良好控制。
OBJECTIVES: To report a clinical syndrome characterized by an increase in progressive motor activity and abnormal changes in the morphology of red blood cells - chiropractic polycythemia. Methods: Review of clinical data in this case, combined with recent literature analysis. Results: The clinical manifestations of this case were various and showed neurological symptoms such as dance movement, hypohylaxis, tics of throat, dystonia, excessive facial motility, cognitive disorders and peripheral nerve damage, and Peripheral blood appears acanthocytosis syndrome characterized by composition. CONCLUSIONS: Avastin, bromocriptine, diazepam, clonazepam and anti-5 HT agents are generally considered ineffective, although no specific therapy is considered effective. However, the efficacy of levodopa and haloperidol is not evaluated. Of the 4 reported cases in the country, 3 (including this case) received good control of recent dance movements and hypohylaxis after oral haloperidol.