本文报告14例肾血管平滑肌脂肪瘤,在形态结构上以成熟的脂肪细胞、厚壁血管和成熟的平滑肌细胞混合组成为其特征。有时,其中可出现一些不成熟的脂肪母细胞、平滑肌母细胞和异型的平滑肌细胞,因而引起误诊。本瘤可独立发生或合并结节性硬化病发生。并发结节性硬化病的病例在我国少 This article reports 14 cases of renal angiomyolipoma, which is characterized by a mixture of mature adipocytes, thick-walled blood vessels and mature smooth muscle cells in the morphological structure. Sometimes, there may be some immature fat cells, smooth muscle cells and abnormal smooth muscle cells, which led to misdiagnosis. The tumor can occur independently or combined with tuberous sclerosis. Concurrent cases of tuberous sclerosis in our country less