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复发性多软骨炎为一罕见的综合征。主要特征为全身软骨组织的变性和炎症,常反复发作,特别多见于眼和耳。目前,文献统计达159例。命名名称繁多。其他常见的名称为慢性萎缩性多软骨炎,多软骨炎,软骨软化,弥漫性软骨炎,弥漫性软骨膜炎,软骨炎及虹膜炎,慢性萎缩性软骨膜炎,家族性慢性萎缩性多软骨炎,软骨溶解性软骨膜炎,风湿性全软骨炎,全软骨炎等。由于本病除有软骨炎外,软骨非软骨结构(如中耳、巩膜、虹膜、主动脉、二尖瓣、心肌、肝、皮肤等)亦有炎症,因此,上述命名均有其局限性。发病率与病程 40～50岁发病率最高,两性发病率无明显差异,发病年龄和性别之间无相互关系。可见于新生儿。欧美各国多见,亚洲、非洲较少见。
Recurrent polychondritis is a rare syndrome. Main features of the body cartilage degeneration and inflammation, often repeated attacks, especially common in the eyes and ears. At present, the literature statistics up to 159 cases. Naming many names. Other common names are chronic atrophic chondritis, polychondritis, chondromalacia, diffuse chondritis, diffuse perichondritis, chondritis and iris, chronic atrophic perichondritis, familial chronic atrophic chondroma Inflammation, cartilage-dissolving perichondritis, rheumatic whole-cartilage, and all-chondritis. Because of the disease except chondritis, cartilage non-cartilage structure (such as the middle ear, sclera, iris, aorta, mitral valve, myocardium, liver, skin, etc.) also have inflammation, therefore, the above naming has its limitations. Incidence and duration of 40 to 50-year-old highest incidence, no significant difference in the incidence of gender, age and gender were not related to each other. Can be seen in newborns. More common in Europe and the United States, Asia, Africa is rare.