成人多囊肾病(adult polycystic kidney disease,APKD)是一种常见的常染色体显性遗传病。它的发病率很高,约1000人中就有一名致病基因的携带者,在美国估计有400 000患者,在英国和其它一些国家,它是约10%末期肾功衰竭和9%肾透析患者的病因。成人多囊肾病发病较晚,一般在30岁以后。男女的发病率无明显差异。病变主要为肾脏和肝脏中的多发性 Adult polycystic kidney disease (APKD) is a common autosomal dominant disease. Its incidence is high, with about one in 1,000 carriers of a disease-causing gene, estimated at 400,000 in the United States, about 10% of end-stage renal failure and 9% of kidney dialysis in the United Kingdom and other countries The cause of the patient. Adult polycystic kidney disease incidence later, usually after the age of 30. The incidence of men and women no significant difference. Lesions are mainly multiple in the kidneys and liver