1961年 Waldmann 首先描述了先天性小肠淋巴发育不良后,至今报道不多,作者报道1例,14岁,男性,腹泻6个月,腹泻与脂肪餐有密切关系,生化检查淋巴细胞减少,严重低蛋白血症,粪便量明显增多,血中α_1-抗胰蛋白酶增高,胃肠钡餐检 Waldmann first described in 1961, congenital small bowel dysplasia, has been reported so far, the authors reported 1 case, 14 years old, male, 6 months of diarrhea, diarrhea and fat meal are closely related to biochemical examination of lymphopenia, severe low Proteins, stool volume increased significantly, blood α_1-antitrypsin increased gastrointestinal barium meal examination