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常染色体显性遗传的成人多囊肾病以发生多发性肾囊肿为其特点。常在四十几岁时引起终末期的肾衰,并为最常见的遗传性肾脏病。Dalgaard估价到80岁为止其发病危险在每10万人中为80—90例,本病占终末期肾病患者中的7％。成人的多囊肾病可能无症状,其表现众多和各不相同。患者有高血压,反复尿路感染,一或二侧腰部的疼痛和包块,因血凝块或结石通过而引起的肾绞痛,肾衰症状,及因囊状血管瘤破裂而引起的蛛网膜下腔出血——一种常与成人多囊肾病有关的异常。
Autosomal dominant adult polycystic kidney disease is characterized by the occurrence of multiple renal cysts. Often in the early forties caused by end-stage renal failure, and is the most common hereditary kidney disease. Dalgaard estimates its risk of developing 80-90 cases per 100,000 people by the age of 80, accounting for 7% of patients with end-stage renal disease. Adult polycystic kidney disease may be asymptomatic, its many manifestations and different. Patients have high blood pressure, recurrent urinary tract infections, pain and mass in one or both lumbar areas, renal colic due to clotting of blood clots or stones, symptoms of renal failure, and spider webs caused by ruptured cystic hemangiomas Subcapsular hemorrhage - a disorder often associated with adult polycystic kidney disease.