大疱性表皮松解症(Epidermolysis Bullosa)是一种少见的先天性疾病,常因轻度外伤即引起大庖发生。1882年Goldscheider氏首先报告,1902年Luithlen氏将其分为单纯型与萎缩型两类。1934年Helitz氏首次发现一新的致死型,患儿多在出生后3个月内死亡,很少能活到8个月,称为致死 Epidermolysis bullosa (Epidermolysis Bullosa) is a rare congenital disease, often due to mild traumatic injury that occurs. Goldscheider’s first report in 1882, 1902 Luithlen’s classification will be divided into two types of simple and atrophy. Helitz’s first discovery in 1934 a new lethal type, most children died within 3 months after birth, rarely survive to 8 months, known as lethal